Presentation
Abdominal pain.
Patient Data
Enhancing mass along rightward aspect of the IVC, growing into it, with a combination of tumor and bland thrombus extending into the right atrium. A shorter segment of bland thrombus in the IVC proximal to the tumor.
Budd Chiari.
PATHOLOGY REPORT
SOURCE OF TISSUE: RETROPERITONEAL MASS ULTRASOUND-GUIDED CORE BIOPSY
FINAL DIAGNOSIS:
Retroperitoneum: Ultrasound-Guided Needle Core Biopsy:
Leiomyosarcoma, IHC: Desmin and SMA positive
Case Discussion
Rare case of biopsy proven inferior vena cava (IVC) leiomyosarcoma. The patient died shortly after admission. The primary mass is along the rightward aspect of the inferior vena cava (extravascular), and extends intravascularly. There is enhancing tumor thrombus and bland thrombus filling the inferior vena cava to the right atrium, resulting in hepatic venous obstruction (Budd Chiari).