Jeune syndrome

Case contributed by Dr Daniel M Conroy


Child admitted with difficulty breathing requiring intubation.

Patient Data

Age: 5 months
Gender: Male
Modality: X-ray

Frontal radiograph showing narrowed shortened ribs and restricted lung volumes.

An enteric tube is also visible.

Post Operative Image

Modality: X-ray

Patient has undergone surgical rib lengthening procedure to improve lung volumes. Bilateral chest drains in-situ.

Case Discussion

This case shows classic features of Jeune syndrome (asphyxiating thoracic dystrophy).

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Case Information

rID: 31887
Case created: 3rd Nov 2014
Last edited: 8th Feb 2017
Inclusion in quiz mode: Included

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