Presentation
Child admitted with difficulty breathing requiring intubation.
Patient Data
Age: 5 months
Gender: Male
From the case:
Jeune syndrome
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Frontal radiograph showing narrowed shortened ribs and restricted lung volumes.
An enteric tube is also visible.
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Patient has undergone surgical rib lengthening procedure to improve lung volumes. Bilateral chest drains in-situ.
Case Discussion
This case shows classic features of Jeune syndrome (asphyxiating thoracic dystrophy).