Jeune syndrome

Case contributed by Dr Daniel M Conroy

Presentation

Child admitted with difficulty breathing requiring intubation.

Patient Data

Age: 5 months
Gender: Male
X-ray

Frontal radiograph showing narrowed shortened ribs and restricted lung volumes.

An enteric tube is also visible.

Post Operative Image

X-ray

Patient has undergone surgical rib lengthening procedure to improve lung volumes. Bilateral chest drains in-situ.

Case Discussion

This case shows classic features of Jeune syndrome (asphyxiating thoracic dystrophy).

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