Presentation
Child admitted with difficulty breathing requiring intubation.
Patient Data
Age: 5 months
Gender: Male
From the case:
Jeune syndrome
Frontal
Frontal radiograph showing narrowed shortened ribs and restricted lung volumes.
An enteric tube is also visible.
Frontal
Patient has undergone surgical rib lengthening procedure to improve lung volumes. Bilateral chest drains in-situ.
Case Discussion
This case shows classic features of Jeune syndrome (asphyxiating thoracic dystrophy).
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