Jeune syndrome

Case contributed by Daniel M Conroy


Child admitted with difficulty breathing requiring intubation.

Patient Data

Age: 5 months
Gender: Male

Frontal radiograph showing narrowed shortened ribs and restricted lung volumes.

An enteric tube is also visible.

Post Operative Image


Patient has undergone surgical rib lengthening procedure to improve lung volumes. Bilateral chest drains in-situ.

Case Discussion

This case shows classic features of Jeune syndrome (asphyxiating thoracic dystrophy).

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