Juvenile dermatomyositis

Case contributed by Dr Ian Bickle

Presentation

Teenager with lethary, lower limb aches and pains. High clinical suspicion of dermatomyositis.

Patient Data

Age: 16
Gender: Male
MRI

Diffuse high T2 signal throughout the musculature of both upper limbs and visualised pelvis.

No muscle group is spared.

Bones normal.

Case Discussion

Juvenile dermatomyositis is a autoimmune inflammatory conditions involving muscles.

The juvenile form has a tendancy to be more severe and is less associated with an underlying malignancy than the adult form.

Auto-antibodies are relatively specific for the condition -- the specific elevated muscle specific antibodies being anti-RNa and anti-Mi2.

This case has the characteristic findings of diffuse high signal throughout affected muscles on T2/TIRM sequences.

 

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Case information

rID: 41207
Case created: 20th Nov 2015
Last edited: 27th Feb 2017
Inclusion in quiz mode: Included

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