Klippel-Trénaunay syndrome

Case contributed by Dr Roberto Schubert

Presentation

Follow up in a known case of Klippel-Trénaunay syndrome.

Patient Data

Age: 25 years
Gender: Male
Photo

Clinical aspect of cutaneous capillary malformations (port wine stains), varicosities, lymphedema and hemihypertrophy of the left lower extremity.

MRI

Complete absence of the left common and external iliac veins. Large, left-to-right crossover anastomosis via the external pudendal veins, sometimes referred to as spontaneous Palma's venous by-pass.

Case Discussion

Combined truncular venous aplasia and hemolymphatic malformation, formerly referred to as Klippel-Trénaunay syndrome.

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Case information

rID: 17495
Published: 18th Apr 2012
Last edited: 7th Jun 2020
System: Vascular
Inclusion in quiz mode: Included