Klippel-Trénaunay-Weber syndrome

Case contributed by Mohammad Farghali Ali Tosson
Diagnosis almost certain

Presentation

Left leg varices

Patient Data

Age: 7 years
Gender: Female

The left femoral vein is attenuated with marked dilatation of the marginal vein of Servelle, which is seen draining into the left common iliac vein associated with multiple dilated superficial tributaries (varicose veins). 

The left common iliac vein is compressed against the lumbar vertebrae by the overlying right common iliac artery with subsequent proximal dilatation.

The well-visualized inferior vena cava (IVC) is average in caliber without intraluminal thrombosis. 

Case Discussion

This is a case of Klippel-Trénaunay-Weber syndrome wherein persistence of the marginal vein of Servelle is a pathognomonic finding.

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