Presentation
Bilateral sensorineural hearing loss.
Patient Data
Age: Child
Gender: Female
From the case:
Large vestibular aqueduct syndrome
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The vestibular aqueducts are bilaterally dilated (more than 3.5 mm in its portion), giving a conical shape appearance.
From the case:
Large vestibular aqueduct syndrome
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MRI axial 3D T2 for the petrous bone revealed dilated vestibular aqueduct and sac bilaterally.
Case Discussion
Large vestibular aqueduct syndrome is the presence of congenital sensorineural hearing loss (SNHL) in combination with an enlarged vestibular aqueduct. It is thought to be one of the most common congenital causes of SNHL.