Large vestibular aqueduct syndrome

Case contributed by Dr Mostafa El-Feky

Presentation

Congenital sensorineural hearing loss (SNHL). She is a candidate for cochlear implant

Patient Data

Age: 15 years
Gender: Female
CT

CT petrous bone

Bilateral large vestibular aqueducts (VAs) and endolymphatic sacs.

The vestibular aqueduct measures 3 mm at the operculum and 1.8 mm at its mid-portion.

MRI

MRI petrous bone

Bilateral large vestibular aqueducts (VAs) and endolymphatic sacs.

Case Discussion

Large vestibular aqueduct syndrome (LVAS) is thought to be one of the most common causes of congenital sensorineural hearing loss (SNHL) and disequilibrium. It is usually sudden after head trauma or progressive during childhood. Cochlear implantation is the surgical effective choice of LVAS if marked hearing loss occurs.

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Case information

rID: 52403
Published: 21st Apr 2017
Last edited: 14th Aug 2019
System: Head & Neck
Inclusion in quiz mode: Included

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