Presentation
Cochlear implant candidate, with bilateral hearing loss.
Patient Data
Age: 20 years
Gender: Female
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Bilateral large vestibular aqueducts (VAs). The VA measures 3 mm at the operculum and 2.5 mm at its mid-portion. Left hearing aid device is noted.
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Bilateral large vestibular aqueducts (VAs) and endolymphatic sacs.
Left choroid fissure cyst is noted.
Case Discussion
Large vestibular aqueduct syndrome (LVAS) is thought to be one of the most common congenital causes of sensorineural hearing loss (SNHL). It is usually sudden after head trauma or progressive during childhood. Cochlear implantation is the surgical effective choice of LVAS if marked hearing loss occurred.