Large vestibular aqueduct syndrome

Case contributed by Dr Mostafa El-Feky

Presentation

Cochlear implant candidate, with bilateral hearing loss.

Patient Data

Age: 20
Gender: Female
CT

Petrous CT

Bilateral large vestibular aqueducts (VAs). The VA measures 3 mm at the operculum and 2.5 mm at its mid-portion. Left hearing aid device is noted.

MRI

Petrous MRI

Bilateral large vestibular aqueducts (VAs) and endolymphatic sacs.

Left choroid fissure cyst is noted.

Case Discussion

Large vestibular aqueduct syndrome (LVAS) is thought to be one of the most common congenital causes of sensorineural hearing loss (SNHL). It is usually sudden after head trauma or progressive during childhood. Cochlear implantation is the surgical effective choice of LVAS if marked hearing loss occurred.

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Case information

rID: 56999
Published: 7th Dec 2017
Last edited: 14th Aug 2019
System: Head & Neck
Inclusion in quiz mode: Included
Institution: Dar El Ashaa Center

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