Large vestibular aqueduct syndrome

Case contributed by Dr Fakhry Mahmoud Ebouda


Sensory neural hearing loss since birth.

Patient Data

Age: 4 years
Gender: Male

Dilated vestibular ducts and sacs bilaterally. Clear middle ear clefts with normal ossicles shape and location as well normal morphology of the oval and round windows.

Dilated vestibular ducts and sacs bilaterally however the vestibule and SCCs as well as cochlear turns with the modiolus show normal morphology and development. 

Case Discussion

Dilated vestibular ducts and sacs bilaterally causing congenital sensory neural hearing loss that resulting in large vestibular aqueduct syndrome.

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Case information

rID: 58915
Published: 12th Mar 2018
Last edited: 14th Mar 2018
Inclusion in quiz mode: Included

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