Presentation
Sensory neural hearing loss since birth.
Patient Data
Age: 4 years
Gender: Male
From the case:
Large vestibular aqueduct syndrome






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Info

Dilated vestibular ducts and sacs bilaterally. Clear middle ear clefts with normal ossicles shape and location as well normal morphology of the oval and round windows.
From the case:
Large vestibular aqueduct syndrome






Download
Info

Dilated vestibular ducts and sacs bilaterally however the vestibule and SCCs as well as cochlear turns with the modiolus show normal morphology and development.
Case Discussion
Dilated vestibular ducts and sacs bilaterally causing congenital sensory neural hearing loss that resulting in large vestibular aqueduct syndrome.