Lipoblastoma

Case contributed by Dr Michael P Hartung

Presentation

Body wall mass with concern for liposarcoma.

Patient Data

Age: 12 months
Gender: Male
CT

6 x 8.5 x 10 cm (AP X TR X CC) fat-containing mass in the right posterior flank. Few areas of mildly thickened septations and stranding; however, the predominant composition of the mass is fat. No discrete rounded soft tissue elements. The mass extends in between and displaces the 11-12th ribs, and to a lesser extent the 10th-11th ribs. No pathologic fracture. The mass distorts the posterior liver capsule and anteriorly displaces the right kidney and retroperitoneum. Loss of tissue plane between the posterior flank/abdominal wall musculature; the latter appears thinned in the areas contacting the mass.

Case Discussion

Large fat-containing mass in the right posterior flank has imaging features most consistent with a lipoblastoma, which is a rare benign mesenchymal tumor which occurs in infancy and early childhood.  Regarding the clinical concern for liposarcoma raised by the ordering team: liposarcomas are extraordinarily rare in patients less than 10 years of age; therefore, a lesion containing fat in a young child is almost invariably a lipoblastoma1.

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Case information

rID: 67022
Published: 17th Mar 2019
Last edited: 5th Apr 2019
System: Paediatrics
Inclusion in quiz mode: Included

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