Lymphangioleiomyomatosis

Case contributed by Dr Lukas Valkovic

Presentation

Recurrent pneumothorax.

Patient Data

Age: 40 years
Gender: Female
CT
  • The initial HRCT demonstrates diffuse cystic changes in both lungs and adhesions in apical regions
  • CT 8 years after initial scan demonstrates marked encapsulated pleural effusions (the mediastinal window images do not show the interval progression of cystic diffuse changes).

VATS was performed with repeated pleurodesis.

MRI

MRI shows multiple confluous retroperitoneal cystic lesions with solid components. 

Case Discussion

The original histology suggested metastatic gynecological origin. After repeated review histology confirmed lymphangioleiomyomatosis.

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Case information

rID: 45448
Published: 25th May 2016
Last edited: 23rd Oct 2020
Inclusion in quiz mode: Excluded

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