Lymphocytic interstitial pneumonia in Sjögren syndrome

Case contributed by Dr Charlie Chia-Tsong Hsu

Presentation

55 year old female with known Sjögren syndrome. Present with longstanding history of dry cough.

Patient Data

Age: 55
Gender: Female

High resolution axial images of the chest demonstrate occasional thin walled cysts (red arrows) measuring up to 1.5 cm in diameter. Note the cysts are peribronchovascular in location and accompanied vessels can often be seen on the walls of the cyst. There are also occasional focal areas of nodular ground glass opacities (blue arrows)  and nodules (green arrow). Coronal minimal intensity projection image demonstrate the basal predominance distribution of disease.

Case Discussion

Lymphocytic interstitial pneumonia in Sjögren syndrome is characterized by lymphocytic infiltration of the small airway or alveolar septa resulting in CT apperance of centrilobular nodules and peribronchiolar ground glass opacities which eventually evolve to form thin walled cysts measuring 5-30 mm. Presence of cysts are useful in differentiating lymphocytic interstitial pneumonia from lymphoma which demonstrate consolidation, larger nodules, or associated pleural effusion.

PlayAdd to Share

Case Information

rID: 23845
Case created: 12th Jul 2013
Last edited: 19th Dec 2015
System: Chest
Inclusion in quiz mode: Included

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.