Madelung deformity
Presentation
Left post-traumatic wrist deformity.
Patient Data
Age: 17
Gender: Female
From the case:
Madelung deformity
X-ray
This is a classic Madelung deformity with :
- Elongated & dorsally subluxated ulna
- Triangularization of the lunate
- Absent sigmoid notch of the distal radius
- Volar tilt of the distal radius
From the case:
Madelung deformity
MRI
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Coronal STIR
MRI shows a partial disruption of the TFCC with ulnar edema, frequently seen in these patient because of intermittent ulnar volar subluxation.
Case Discussion
Madelung deforrmity is associated with:
- Leri-Weill syndrome : an autosomal dominant dyschondrosteosis (a form of mesometric dwarfism)
- Turner syndrome
- Madelung dyschondrosteosis
- gonadal dysgenesis
- nail-patella syndrome
- diaphyseal aclasis (hereditary multiple exostosis)
- Hurler mucopolysaccharidosis
- achondroplasia
- Ollier disease
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