Madelung's dyschondrosteosis

Case contributed by Dr Wael Nemattalla

Presentation

Bilateral arm deformities and short stature.

Patient Data

Age: 17 years
Gender: Female
X-ray

There were symmetrical arm bone findings; the left is presented. X-ray of legs [not shown] showed bilateral symmetrical upper tibial and fibular deformities with medial inclinations.

Note:

  1. Decreased carpal angle [normal between 118° and 139°].
  2. V-shaped carpal angle.
  3. Herniation of proximal carpal row of bones.
  4. Dysplastic proximal radius with shortening which is characteristic of Madelung's dyschondrosteosis rather than the primary Madelung's deformity.

Case Discussion

Note:

  1. Decreased carpal angle [normal between 118° and 139°].
  2. V-shaped carpal angle.
  3. Herniation of proximal carpal row of bones.
  4. Dysplastic proximal radius with shortening which is characteristic of Madelung's dyschondrosteosis rather than the primary Madelung's deformity.
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Case information

rID: 8824
Published: 1st Mar 2010
Last edited: 13th Aug 2019
Inclusion in quiz mode: Included

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