Malrotated duplex kidney

Case contributed by Dr Matthew Lukies


Abdominal pain for investigation on background of hypertrophic obstructive cardiomyopathy (HOCM)

Patient Data

Age: 20 years old
Gender: Male
  • Single lead pacemaker in situ
  • No cause for the patient's abdominal pain identified
  • Incidental finding of an anterolaterally facing malrotated duplex left kidney, with a duplex collecting system draining into a single ureter
  • Two left renal arteries, with the inferior artery arising from the left common iliac artery and passing posterior to the kidney
  • Three left renal veins, one passing anterior to the aorta and draining into the right IVC, one joining a left ascending lumbar vein and passing retroaortic into the IVC, and one passing posterior to the kidney to drain into the left common iliac vein
  • Two right renal arteries and two right renal veins

Case Discussion

In this case, the duplex collecting system unites into a single ureter at the pelviureteric junction (PUJ), but a duplex collecting system may have two ureters that unite before the vesicoureteric junction (VUJ), called bifid ureter, or complete duplication, called double ureter.

The renal malrotation in this case would be classified as incomplete, with the hilum and pelvis facing anterolaterally. This is the most common type of renal malrotation, but the renal hilum may face posteriorly (excessive rotation) or further laterally (reversed rotation).


Case findings a collective effort with thanks to Dr Alex Jarema and Dr George Harisis.

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Case information

rID: 45697
Published: 4th Jun 2016
Last edited: 6th Jun 2016
System: Urogenital
Inclusion in quiz mode: Included

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