Low back pain, urinary incontinence.
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- Extensive aortic root dilatation measuring up to 9.6 cm regarding its maximum dimensions as well as the sino-tubular junction, this is associated with lumbosacral dural ectasia manifested as scalloping of the dorsal surface of the vertebrae with pre-sacral and lateral sacral meningioceles.
- Gross cardiomegaly.
- Normal caliber of the ascending, arch and descending thoracic aorta, with no stenotic or dilated segments. The visceral branches of the arch of aorta (left subclavian, left common carotid and brachiocephalic arteries) are patent showing normal course and caliber. No evidence of aneurysmal dilatation. No dissection flap seen.
- Normal caliber of the supra and infra-renal abdominal aorta, with no stenotic or dilated segments. The visceral branches of the abdominal aorta (celiac trunk and inferior mesenteric arteries) are patent showing normal course and caliber.
The findings on this CT that suggests Marfan syndrome as the unifying diagnosis include:
- diffuse dural ectasia
- enlarged sacral foramina, presacral and lateral sacral meningocoele with scalloping of the dorsal surface of vertebral bodies
- dilated aortic root with multichamber gross cardiac enlargement and passive congestive hepatomegaly