Massive ascending thoracic aortic aneurysm

Case contributed by Dr Michael P Hartung

Presentation

Congestive heart failure.

Patient Data

Age: 35 years
Gender: Male

Massive fusiform ascending aortic aneurysm involving the root/sinuses of Valsalva, 8.8 cm AP. 

Left ventricular dilation. 

Brachiocephalic ectasia. 

Case Discussion

While undiagnosed, this patient almost certainly has an underlying connective tissue disorder to account for the formation of his massive aneurysm at such a young age (such as Marfan, Ehlers Danlos, or Loeys Dietz1). No evidence of rupture. Ectasia of the brachiocephalic artery supports a connective tissue disorder. 

For aneurysm greater than 6 cm, the risks are as follows:

  • rupture 3.7% per year
  • rupture or dissection at 6.9% per year
  • death at 11.8%
  • and death, rupture, or dissection at 15.6% per year2
PlayAdd to Share

Case information

rID: 73839
Published: 27th Jan 2020
Last edited: 29th Jan 2020
System: Vascular
Inclusion in quiz mode: Included
Institution: Tenwek Hospital

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.