Mayer-Rokitansky-Küster-Hauser syndrome

Case contributed by Dr Erik Ranschaert

Presentation

22-year old woman without menstruation and dyspareunia.

Patient Data

Age: 22
Gender: Female

The patient has no uterus and no distinct vagina. The right adnex contains several follicles.

Case Discussion

The Mayer-Rokitansky-Küster(-Hauser) Syndrome (MRK or MRKH) presents a congenital female anomaly with agenesis of the uterus. It belongs to the Mullerian duct anomalies

The patient does have normal adnexa and no further renal anomalies, except for a double excretory system on the left side.

Therefore this patient is considered to have the typical form (type A) of this syndrome characterized by congenital absence of the uterus and upper vagina with normal ovaries and fallopian tubes.

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Case information

rID: 12340
Case created: 11th Nov 2010
Last edited: 3rd Sep 2017
Inclusion in quiz mode: Included

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