Mayer-Rokitansky-Küster-Hauser syndrome (MRKH)

Case contributed by Dr Ammar Haouimi


Primary amenorrhea.

Patient Data

Age: 15 years
Gender: Female

The MRI sequences demonstrate;

  • absence of the uterus
  • vaginal agenesis
  • ovaries well-visualized in the iliac fossae with small follicles
  • single, malrotated left pelvic kidney with compensatory hypertrophy

Case Discussion

MRI features of Mayer-Rokitansky-Küster-Hauser syndrome with single malrotated left pelvic kidney (atypical form or type B).

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