Presentation
Primary amenorrhea.
Patient Data
Age: 15 years
Gender: Female
From the case:
Mayer-Rokitansky-Küster-Hauser syndrome (MRKH)
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The MRI sequences demonstrate;
- absence of the uterus
- vaginal agenesis
- ovaries well-visualized in the iliac fossae with small follicles
- single, malrotated left pelvic kidney with compensatory hypertrophy
Case Discussion
MRI features of Mayer-Rokitansky-Küster-Hauser syndrome with single malrotated left pelvic kidney (atypical form or type B).