Mayer-Rokitansky-Küster-Hauser syndrome (MRKH) with a tailgut cyst

Case contributed by Dr Ammar Haouimi


Primary amenorrhea

Patient Data

Age: 25 years
Gender: Female

The uterus is not visualized as well as the fallopian tubes with no distinct vagina. Both ovaries are well-visualized, containing several follicles.

The left lumbar fossa is occupied by the spleen and the left kidney is in an ectopic position in the left pelvic region.

A multiloculated cystic mass is seen in the retrorectal space, suggestive of a tailgut cyst.

No sacrococcygeal abnormalities are seen.

Case Discussion

Mayer-Rokitansky-Küster-Hauser syndrome belongs to class I Mullerian duct anomalies 

Associated renal anomalies may be seen up to 30-40% of cases, but tailgut cyst is rarely associated with uterine anomalies.

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Case information

rID: 63336
Published: 1st Oct 2018
Last edited: 6th Oct 2018
System: Gynaecology
Inclusion in quiz mode: Included
Institution: Aurès Medical Imaging Center - Batna Algeria

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