Mayer-Rokitansky-Küster-Hauser syndrome (MRKH) with rudimentary uterine horns

Case contributed by Ammar Haouimi
Diagnosis almost certain

Presentation

Primary amenorrhea.

Patient Data

Age: 20 years
Gender: Female

Rudimentary uterine horns with a soft tissue band connecting both uterine horns. No visualization of the uterine body, cervix or vagina.

Both ovaries are well developed, showing numerous follicles largest on the right.

Both kidneys were normal on the ultrasound exam (not shown).

 

Case Discussion

MRI features of a Mayer Rokitansky Kuster Hauser syndrome (MRKH) with bilateral rudimentary uterine horns which is considered a rare form.

 

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.