Mayer-Rokitansky-Küster-Hauser syndrome (MRKH) with rudimentary uterine horns
Diagnosis almost certain
Presentation
Primary amenorrhea.
Patient Data
Age: 20 years
Gender: Female
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Rudimentary uterine horns with a soft tissue band connecting both uterine horns. No visualization of the uterine body, cervix or vagina.
Both ovaries are well developed, showing numerous follicles largest on the right.
Both kidneys were normal on the ultrasound exam (not shown).
Case Discussion
MRI features of a Mayer Rokitansky Kuster Hauser syndrome (MRKH) with bilateral rudimentary uterine horns which is considered a rare form.