McCune-Albright syndrome - fibrous dysplasia

Case contributed by Dr Andrew Dixon

Presentation

Known facial disorder. Pre-operative planning.

Patient Data

Age: 40
Gender: Female

CT of the facial skeleton of a 40 year old woman demonstrates extensive bony expansion with areas of heterogeneous bone density ranging from sclerotic to lucent. The majority of affected bones demonstrate a ground-glass appearance.

Nuclear medicine

Bone scan demonstrates extensive craniofacial uptake as well as involvement of a single right sided rib.

Case Discussion

CT of the facial skeleton of a 40 year old woman demonstrates extensive bony expansion with areas of heterogeneous bone density ranging from sclerotic to lucent. The majority of affected bones demonstrate a ground-glass appearance.

Bone scan demonstrates extensive craniofacial uptake as well as involvement of a single right sided rib.

Features are consistent with  craniofacial fibrous dysplasia. Presence of rib involvement and acromegaly is consistent with the patient's known McCune-Albright syndrome.

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Case information

rID: 9550
Published: 28th Apr 2010
Last edited: 22nd Oct 2018
Inclusion in quiz mode: Included

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