Presentation
Patient was brought for investigation due to deafness since birth.
Patient Data
Age: 2 years
Gender: Male
From the case:
Michel (complete labyrinthine) aplasia
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The brain window shows normal brain development.
Axial and coronal high-resolution CT imaging shows complete absence of differentiated inner ear structures. The middle ear and external auditory meatus are normal.
Case Discussion
Michel aplasia (complete labyrinthine aplasia) is a rare congenital anomaly characterized by total absence of inner ear structure developments bilaterally thus leading to anacusis.
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