Mondini malformation

Case contributed by A.Prof Frank Gaillard


Hearing loss bilaterally; Sensorineural loss on audiometry. No discharge.

Patient Data

Age: 6
Gender: Male

Cochlea has 1.5 turns instead of usual 2.5 turns bilaterally; Dilated vestibular aqueduct as well as horizontal semicircular canals.

Case Discussion

Mondini malformation (bilateral) as seen in this case, is a common cause of congenital sensorineural hearing loss. Since basal turns are intact, hearing would not be however completely lost, and it would be purely sensorineural.

PlayAdd to Share

Case information

rID: 5590
Case created: 13th Feb 2009
Last edited: 9th Dec 2015
System: Head & Neck
Inclusion in quiz mode: Included

Updating… Please wait.

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.