Moya moya disease

Case contributed by Dr Andrew Dixon

Presentation

One week history of left-sided weakness.

Patient Data

Age: 3 years
Gender: Female
MRI

MRI brain

The supraclinoid ICA and P1 segments of the PCA are occluded with large perforator collaterals. A number of basal ganglia infarcts are noted on DWI. 

DSA (angiography)

Angiogram confirms extensive perforator colaterals giving the 'puff of smoke' characteristic of this disease, and involving both anterior and posterior circulation. 

Case Discussion

Typical features of moya moya disease in the typical age group, and presenting in the typical fashion for this age group - namely infarcts. 

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Case information

rID: 10586
Published: 23rd Aug 2010
Last edited: 5th Sep 2019
Inclusion in quiz mode: Included

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