Moya moya with hemorrhage

Case contributed by A.Prof Frank Gaillard

Presentation

Acute deterioration in conscious state. No known history of hypertension.

Patient Data

Age: 70 years
Gender: Female
CT

Large hemorrhage is noted arising in the parenchyma near the caudate head on the left side, inferiorly reaching the interhemispheric fissure and superiorly entering the ventricles. Vast amounts of intraventricular hemorrhage are present with hydrocephalus. 

CT

CT angiography

CTA demonstrates bilateral supraclinoid ICA occlusion with large bilateral lenticulostriate collaterals. 

Case Discussion

It is important to remember that Moya-moya pattern is seen in a variety of contexts. Moya moya disease is, in contrast, idiopathic and seen primarily in children. When complications arise they can be fairly well predicted by the patient's age. Children typically suffer from ischemic events, whereas adults tend to present with hemorrhages from the lenticulostriate collateral vessels. 

PlayAdd to Share

Case information

rID: 46190
Published: 26th Jun 2016
Last edited: 14th Aug 2019
Inclusion in quiz mode: Included

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.