Moyamoya disease

Case contributed by Utkarsh Kabra
Diagnosis almost certain

Presentation

Right sided weakness.

Patient Data

Age: 4 years
Gender: Female
mri

Multiple gliotic areas involving bilateral frontoparietal lobes. Small gliotic areas in bilateral centrum semiovale. Small chronic infarcts in right basal ganglia.

Subtle linear hyperintensities along the sulci bilaterally.

Multiple tortuous flow voids in bilateral basal cisterns, suprasellar cistern and along convexity sulci representing collateral vessels.

Mild asymmetry of lateral ventricles is seen with mild prominence of right
lateral ventricle.

Gross narrowing of supraclinoid segments of both internal carotid arteries with multiple prominent lenticulostriate, thalamostriate, leptomeningeal and dural collaterals.

Case Discussion

Findings are characteristic of moyamoya disease

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