Note: This case has been tagged as "legacy" as it no longer meets image preparation and/or other case publication guidelines.
DSA vertebrobasilar system: note the occluded posterior cerebral arteries bilaterally.
DSA right ICA: markedly stenosed distal Rt ICA with neovascular tufts.
DSA left ICA: occluded left ICA.
Bilateral watershed infarcts
Case Discussion
Moyamoya disease is a vasculo-occlusive disease involving the circle of Willis, typically the terminal ICA.
The term moyamoya disease should be reserved for an idiopathic, sometimes familial, condition, which leads to characteristic intracranial vascular changes. Numerous entities have been described which mimic the appearance, in which case the term moyamoya phenomenon, syndrome or pattern is used.