Moyamoya pattern

Case contributed by Assoc Prof Frank Gaillard
DSA (angiography)

DSA vertebrobasilar system: note the occluded posterior cerebral arteries bilaterally.

DSA  right ICA: markedly stenosed distal Rt ICA with neovascular tufts. 

DSA left ICA: occluded left ICA.


Bilateral watershed infarcts

Case Discussion

Moyamoya disease is a vasculo-occlusive disease involving the circle of Willis, typically the terminal ICA. 

The term moyamoya disease should be reserved for an idiopathic, sometimes familial, condition, which leads to characteristic intracranial vascular changes. Numerous entities have been described which mimic the appearance, in which case the term moyamoya phenomenon, syndrome or pattern is used. 

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Case information

rID: 2633
Published: 7th May 2008
Last edited: 30th Nov 2019
Inclusion in quiz mode: Excluded

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