Moyamoya syndrome (with background sickle cell disease)

Case contributed by Dr Kauv Paul

Presentation

Follow up in patient with sickle cell disease.

Patient Data

Age: 30

There is no flow in cavernous segment of the right ICA with reconstitution of the flow in supraclinoid segment and distal branches. There is also narrowing of the supraclinoid segment of the left ICA and MCAs bilaterally with reduced number and calibre of the cortical branches of MCAs. Vertebrobasilar system is relatively spared.
There is network of multiple small collateral branches at the base of the brain, ambient cisterns and also intraaxial bilateral basal ganglia region in keeping with moyamoya collaterals.  

Case Discussion

Moyamoya syndrome in a patient with sickle cell disease and with evidence of chronic ischaemia in cortical watershed zones in deep corona radiata regions.

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Case information

rID: 35534
Case created: 9th Apr 2015
Last edited: 10th Sep 2015
Inclusion in quiz mode: Included

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