Neurofibromatosis type 2 - with multiple meningiomas

Case contributed by Bruno Di Muzio
Diagnosis almost certain

Presentation

Known history of NF2. Previous cerebral surgery for a tumor resection.

Patient Data

Age: 65 years
Gender: Female

All the lesions are stable compared to the previous MRI. Multiple extra-axial solid tumors at strongly suggest meningiomas are again identified in: the right CPA protruding over the ipsilateral VII and VIII cranial nerves, adjacent to the tentorium on the left, in the left occipital, occipito-parietal and parietal regions, and in the left middle cranial fossa. The left solid nodule within the vestibulocochlear nerve can represent a schwannoma. 

Case Discussion

Neurofibromatosis type 2 is a rare autosomal dominant phakomatosis manifesting as development of multiple CNS tumors. Unlike neurofibromatosis type 1 (NF1), it is not associated with neurofibromas.  Instead, patients with this disease have:

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