Multiple system atrophy

Case contributed by Dr Andrew Lawson

Presentation

Progressive ataxia.

Patient Data

Age: 45
Gender: Female
MRI

There is marked atrophy of the pons, midbrain, middle cerebellar peduncles and cerebellum diffusely. In addition there is central pontine signal abnormality is present conforming to the so-called "hot cross bun sign".  No other focal abnormality identified. Supratentorial cerebral volume is age appropriate. Mesial temporal lobes appear normal. No intracranial mass, collection, evidence of restricted diffusion, or perfusion abnormality.

Case Discussion

 Findings are consistent with olivopontocerebellar atrophy (also known as MSA-C).
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Case information

rID: 25634
Case created: 1st Nov 2013
Last edited: 24th Sep 2015
Inclusion in quiz mode: Included

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