Neuro-Behçet disease

Case contributed by Dr Dalia Ibrahim

Presentation

Recurrent attacks of aphasia, diplopia and bilateral lower limb weakness.

Patient Data

Age: 30 years
Gender: Male
MRI

Abnormal signal of the midbrain, pons, middle cerebellar peduncles and anterior medulla.

Left basal ganglia multiple small foci of CSF like signal, likely chronic ischemic foci.

Bilateral high parietal multiple subcortical patches of abnormal signal.

Case Discussion

The patient has a history of Behçet disease.

Behçet disease (BD) is a multisystem vasculitis of unknown origin.

Neurologic involvement includes typical and atypical parenchymal neuro-Behçet disease, dural sinus thrombosis, cerebral arterial aneurysm, occlusion, dissection, and meningitis

Parenchymal neuro-Behçet primarily affects the brainstem (especially the mesodiencephalic junction, around the cerebral peduncles and the pons) or the basal ganglia, thalami, or subcortical white matter.

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Case information

rID: 57512
Published: 29th Dec 2017
Last edited: 16th Jul 2018
Inclusion in quiz mode: Included

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