Presentation
Left side weakness. Disphagia. Recurrent uveitis. Patient diagnosed with Behçet disease 3 years ago.
Patient Data
T2W hyperintense lesion infiltrates the pons extensively and elongates to the both crus cerebries and middle cerebellar pedincules. There were smooth rim and nodular contrast enhancements within the lesion. In T2 hyperintense lesion, isointense points belong to spared axons can be seen like tigroid patern. In the right temporal lobe, gliosis can be seen related to the priory operation about meningioma.
Case Discussion
Neuro-Behçet disease is central nervous system manifestations of Behçet disease.
Lesions in Neuro-Behçet disease typically involve the brainstem (most common in the pons), basal ganglia, thalamus, less common subcortical white matter and spinal cord.
Lesions typically demonstrate the following signal characteristics:
- T1: usually hypointense
- T2: usually hyperintense, associated with vasogenic edema
- T1 C+(Gd): typically moderate patchy enhancement
- DWI: isointense to slightly hyperintense