Neurosarcoidosis and Chiari I malformation

Case contributed by A.Prof Frank Gaillard

Presentation

Ataxia.

Patient Data

Age: 18 years
Gender: Female

MRI brain

Modality: MRI

Extensive oedema and enhancement of the surface of the left cerebellar hemisphere are noted with additional enhancement of the pons. The cerebellar tonsils are low lying by ~12 mm, reaching below the posterior arch of C1. 

Modality: MRI

MRI of the cervical spine demonstrates extensive syrinx without enhancement associated with a prominent chiari I malformation. 

Case Discussion

This patient went on to have a posterior fossa decompression and biopsy of her posterior fossa meninges which revealed granulomatous inflammation compatible with sarcoidosis. This was confirmed clinically. 

PlayAdd to Share

Case Information

rID: 4364
Case created: 14th Aug 2008
Last edited: 17th Oct 2015
Inclusion in quiz mode: Included

Updating… Please wait.
Loadinganimation

Alert accept

Error Unable to process the form. Check for errors and try again.

Alert accept Thank you for updating your details.