Open lip schizencephaly
Enlarged head and suspected hydrocephalus. Very large right lateral ventricle on ultrasound (not shown). MRI was recommended for further evaluation.
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A very large cleft joining the sub-arachnoid space with the body of the right lateral ventricle. The cleft is lined by gray matter. Absent suptum pellucidum.
The findings are consistent with open lipped schizencephaly. Absence of the septum pellucidum is a known association.
If the cleft is not lined by gray matter, then a differential diagnosis should include porencephalic cyst.
- Abdel Razek AA, Kandell AY, Elsorogy LG et-al. Disorders of cortical formation: MR imaging features. AJNR Am J Neuroradiol. 2008;30 (1): 4-11. doi:10.3174/ajnr.A1223 - Pubmed citation
- Edris F, Kielar A, Fung KF et-al. Ultrasound and MRI in the antenatal diagnosis of schizencephaly. J Obstet Gynaecol Can. 2009;27 (9): 864-8. Pubmed citation