Osler-Weber-Rendu syndrome

Case contributed by Dr Ahmed Abd Rabou

Presentation

Abnormal chest radiograph for a patient with recurrent hemoptysis

Patient Data

Age: 25 years old
Gender: Male
CT

Scout image revealed two well defined nodules, one at the right lower lung zone lobulated in shape and the other one rounded at left lower lung zone. At least two arteriovenous malformations with feeding vessels are noted at posterior basal segment of right lower lobe giving the appearance of comma shape nodules. Another similar one seen at left lower lobe.

Annotated image

Hepatic AVM in subsegment VIII (red circle)

Case Discussion

The patient has multiple arteriovenous malformation in the nasal and oral mucosa, lungs and liver. Cerebral angiography ruled out cerebral AVMs. The patient was diagnosed Hereditary Hemorrhagic Telangectasia and coiling of pulmonary AVMs is on the treatment plan.

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Case information

rID: 30110
Case created: 19th Jul 2014
Last edited: 9th Mar 2017
System: Chest
Inclusion in quiz mode: Included

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