Partial anomalous pulmonary venous return

Case contributed by Dr M Sanal Kumar

Presentation

Asymptomatic patient. Came for health check up. Routine chest radiograph was taken.

Patient Data

Age: 36
Gender: Male
Modality: X-ray

There is hypoplasia of the right lung and dextroposition of the heart.

Mediastinal shift to the right side and also right diaphragmatic elevation also noted.

Anomalous (scimitar) vein paralleling right heart border.

 

Constellation of findings are suggestive of partial anomalous pulmonary venous return Scimitar's syndrome.

 

Case Discussion

Hypogenetic Lung (Scimitar) Syndrome

  • 4 features typical (although each not always present):
  • hypoplasia of the lung with abnormal segmental or lobar anatomy
  • hypoplasia of the ipsilateral pulmonary artery
  • anomalous pulmonary venous return (scimitar vein)
  • anomalous systemic arterial supply to lower lobe

Other features:

  • almost always on the right sidem
  • mediastinal shift toward the hypoplastic lung
  • reduced size of ispilateral pulmonary artery
  • anomalous (scimitar) vein usually paralleling right heart border
  • congenital heart disease in 25% (e.g., atrial septal defect and patent ductus arteriousus)

Clinical symptoms: recurrent infection and dyspnea.

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Case Information

rID: 35312
Case created: 31st Mar 2015
Last edited: 5th Dec 2015
Inclusion in quiz mode: Included

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