Persistent hyperplastic primary vitreous

Case contributed by Fakhry Mahmoud Ebouda
Diagnosis certain

Presentation

Left globe is relatively smaller than the right with white pupil since birth.

Patient Data

Age: 3 years.
Gender: Female

The left eye appears relatively smaller than the right (microphthalmia). Presence of a retrolental soft tissue along the Cloquet canal owing to persistence of remnant of hyaloid vessels.

 

Case Discussion

Persistent hyperplastic primary vitreous and retinoblastoma are on the top differential of leukocoria as well as microphthalmos.

The MRI is planned to demonstrate other associated congenital anomalies.

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