Pleuropulmonary blastoma

Case contributed by Dr Riyad Waheed Alesawi

Presentation

Shortness of breath and weight loss.

Patient Data

Age: 5 years
Gender: Female

A large heterogeneous tumor mass with central calcification is seen occupying the left hemithorax. It shows heterogeneous contrast enhancement. It is occupying most of the left hemithorax partially sparing the lung apex with displacement of mediastinum to right side. No bone destruction.

Tru cut biopsy confirming the diagnosis of pleuropulmonary blastoma.

Case Discussion

Primary lung malignancies are exceedingly rare in children, with an incidence of approximately 0.05 per 100,000. The most common tumors are pleuropulmonary blastoma, bronchogenic carcinoma and bronchial adenoma

In our case, we put pleuropulmonary blastoma at the top of differential diagnosis and was confirmed on histopathology. 

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