Plexiform neurofibroma

Case contributed by Dr Lukas Valkovic


Slow growing masses on the neck with multiple resections done over 4 decades.

Patient Data

Age: 65 years
Gender: Male

There are multiple confluent enhancing lesions predominantly on the left side of the neck and in the upper mediastinum which are responsible for an asymetrical stenosis of the pharynx and trachea. Notice the target sign on T2 sequence typical for neurofibromas. 

Case Discussion

This patient underwent several surgical resections throughout last decades (and also recent chemotherapy treatment) with histologically confirmed diagnosis of plexiform neurofibroma (see article Neurofibromatosis type I). There were also signs of malignant transformation documented. 

How to use cases

You can use Radiopaedia cases in a variety of ways to help you learn and teach.

Creating your own cases is easy.

Updating… Please wait.

 Unable to process the form. Check for errors and try again.

 Thank you for updating your details.