Plexiform neurofibroma

Case contributed by Dr Abiola Ayodele

Presentation

Craniofacial plexiform neurofibromas in a known neurofibromatosis type 1 patient.

Patient Data

Age: 15 years
Gender: Male
MRI

There are extensive plexiform neurofibromas seen in the subcutaneous layer of the face, scalp, masticator spaces, parotid spaces, carotid spaces and the orbits. There is associated proptosis of the right globe. The lesions appear isointense on T1, heterogeneously enhancing on gadolinium administration and demonstrate the typical target appearance on T2/FLAIR sequences.

Cortical atrophy is also noted, worse on the right.

Case Discussion

Typical MRI findings of plexiform neurofibroma in neurofibromatosis type 1.

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Case information

rID: 89012
Published: 28th Apr 2021
Last edited: 30th Apr 2021
System: Head & Neck
Inclusion in quiz mode: Included
Institution: Lagos state university teaching hospital

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