Presentation
Abdominal pain.
Patient Data
Multiple thin walled cysts of varying sizes are present throughout the liver without apparent biliary tree dilatation. The giant cyst measures about 90 mm in diameter.
A 60 mm simple cortical cyst is present at the lower pole of the left kidney.
Additionally, a few small cortical cysts are scattered at the kidneys.
Case Discussion
Features on MRI are most compatible with polycystic liver disease (PCLD), which is a hereditary condition. 75-90% of patients with autosomal dominant polycystic kidney disease have PCLD, and PCLD without ADPKD has a prevalence of <0.01%.
Most patients are asymptomatic, but occasionally patients can have pain with large cysts.