Polymicrogyria and absent septum pellucidum
Citation, DOI, disclosures and case data
At the time the case was submitted for publication Ian Bickle had no recorded disclosures.View Ian Bickle's current disclosures
Middle aged man with 17 year history of epilepsy. Previous CT 10 years ago apparently normal.
Loading Stack -
0 images remaining
Moderate degree of right perisylvian polymicrogyria. No schziencephaly.
Absent septum pellucidum giving a 'mono-ventricle' appearance, with a normal appearing optic chiasm and no hypotelorism.
Left hemisphere normal. Posterior fossa normal.
MRI is now almost routinely performed in those with epilepsy to review for an underlying structural abnormality responsible for seizures.
One of the key elements to be reviewed is the presence of a wide range of cortical dysplasias and migrational disorders. In this case polymicrogyria is found in the most commonly affected area, the perisylvian region, and is associated with an absent septum pellucidum, which is a recognized association.
This is an exceptionally late presentation on MRI, which is likely related to local circumstances and limited access to MRI.
2 articles feature images from this case
16 public playlists include this case
- my 2B Cases by Tamer
- Absent Septum Pellucidum by Audrey Pinna
- Pediatric by Marta Aguilar Perez
- VIVA by R A A
- Paeds Tute by anthony trimboli ◉
- FRANZCR 01A Neuro by AMIRSALEH JAFARI
- CNS 2b by Mohamed Talaat
- YJL 2B Neuro by YJ Lee
- Mri head by N Seth
- NeuroradiologyRIPAS - teaching cases by Ian Bickle ◉
- Neuroanatomy by Muhammad AlMatter
- Paeds Prac WA by Chandra
- Neuro by Diego González
- Miscellanea by Marta Aguilar Perez
- FRANZCR 05 Paediatrics by AMIRSALEH JAFARI
- Brain-1 by Ismail Sayed Ismail