Presentation
Crohn disease with a history of splenectomy presented for follow-up.
Patient Data
Cavernomatous transformation of the portal vein, with minimal intrahepatic biliary dilatation.
Cavernomatous transformation of the portal vein, with minimal intrahepatic biliary dilatation.
Case Discussion
Portal biliopathy is defined as biliary obstruction with enlarged collateral veins as a consequence to chronic portal vein occlusion.
The smooth appearance of the stenosis has been described as pseudosclerosing cholangitis or pseudocholangiocarcinoma 1.
The concomitant findings of Crohn disease is out of the scope of this description.