Post hemispherectomy for Rassmussen encephalitis

Case contributed by Dr Chris O'Donnell

Presentation

Seizures and twitching. PH of hemispherectomy for Rassmussen encephalitis as a child. Long standing right hemiplegia but otherwise functioning normally.

Patient Data

Age: 20
Gender: Male

Absence of the left cerebrum apart from the basal ganglia.  Note atrophy of the left cerebral peduncle (arrow) and filling of the left hemicranial space by CSF.

Case Discussion

This radical surgery is rarely performed in childhood for developmental lesions (mostly extensive cortical dysplasias), acute pathologies such as MCA infarct or trauma and progressive pathology such as Rasmussen encephalitis and Sturge-Weber syndrome. Despite the almost inevitable development of hemiplegia, most children have an excellent long-term outcome with reduction or absence of seizures, and normal intellectual function and speech.

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Case information

rID: 47095
Case created: 31st Jul 2016
Last edited: 1st Aug 2016
Inclusion in quiz mode: Excluded

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